Title Surgical management of adult Hirschsprung’s disease by subtotal colectomy: a possible alternative /
Translation of Title Suaugusiųjų Hirschprungo ligos chirurginis gydymas subtotaline kolektomija: galima alternatyva.
Authors Kildušis, Edvinas ; Poškus, Tomas ; Strupas, Kęstutis
DOI 10.15388/LietChirur.2016.4.10280
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Is Part of Lietuvos chirurgija.. Vilnius : Vilniaus universiteto leidykla. 2016, t. 15, Nr. 4, p. 162-164.. ISSN 1392-0995. eISSN 1648-9942
Keywords [eng] adult Hirschsprung’s disease ; constipation ; megacolon ; aganglionosis
Abstract [eng] Adult Hirschsprung’s disease (AHD) is a rare and often undiagnosed condition. At present, only a limited number of cases have been reported. We managed a 19-year-old woman with rich history of chronic constipation and abdominal discomfort. Abdominal radiography and barium enema examination demonstrated massively dilated colon (up to 15 cm in diameter). Full-thickness rectal biopsy showed absence of ganglionic cells. AHD was diagnosed and subtotal colectomy with ileorectal anastomosis was performed. At five-year follow up, the patient had significantly improved defecation and quality of life and was extremely satisfied with the operation. AHD should be considered in patients with long-standing and refractory constipation with megacolon. We advocate a subtotal colectomy with ileorectal anastomosis as one of the possible surgical alternatives in such young patients.
Published Vilnius : Vilniaus universiteto leidykla
Type Journal article
Language English
Publication date 2016
CC license CC license description