Title |
Surgical management of adult Hirschsprung’s disease by subtotal colectomy: a possible alternative / |
Translation of Title |
Suaugusiųjų Hirschprungo ligos chirurginis gydymas subtotaline kolektomija: galima alternatyva. |
Authors |
Kildušis, Edvinas ; Poškus, Tomas ; Strupas, Kęstutis |
DOI |
10.15388/LietChirur.2016.4.10280 |
Full Text |
|
Is Part of |
Lietuvos chirurgija.. Vilnius : Vilniaus universiteto leidykla. 2016, t. 15, Nr. 4, p. 162-164.. ISSN 1392-0995. eISSN 1648-9942 |
Keywords [eng] |
adult Hirschsprung’s disease ; constipation ; megacolon ; aganglionosis |
Abstract [eng] |
Adult Hirschsprung’s disease (AHD) is a rare and often undiagnosed condition. At present, only a limited number of cases have been reported. We managed a 19-year-old woman with rich history of chronic constipation and abdominal discomfort. Abdominal radiography and barium enema examination demonstrated massively dilated colon (up to 15 cm in diameter). Full-thickness rectal biopsy showed absence of ganglionic cells. AHD was diagnosed and subtotal colectomy with ileorectal anastomosis was performed. At five-year follow up, the patient had significantly improved defecation and quality of life and was extremely satisfied with the operation. AHD should be considered in patients with long-standing and refractory constipation with megacolon. We advocate a subtotal colectomy with ileorectal anastomosis as one of the possible surgical alternatives in such young patients. |
Published |
Vilnius : Vilniaus universiteto leidykla |
Type |
Journal article |
Language |
English |
Publication date |
2016 |
CC license |
|