| Abstract [eng] |
Objective: the World Health Organization reports that around 5% of the global population, which is approximately 430 million people, have some degree of hearing impairment and require assistive devices. In developed countries, hereditary hearing loss accounts for almost 60% of deafness cases and about 30% of those cases are associated with syndromes. Congenital syndromes that cause malformations of the face and head can lead to damage in the outer and inner ear structures, resulting in various degrees of hearing impairment either in early childhood or later in life. Aim: to review various syndromes that present with craniofacial malformations and hearing loss to determine the most common type of hearing loss and its mechanism. Methods: a descriptive literature review was conducted using keywords in the PubMed and Google Scholar databases. Conclusion: in cases of craniofacial malformations, hearing impairment of the conduction type is most common and typically detected due to issues such as otitis media with effusion, changes in the external auditory canal, dysfunction of the Eustachian tube, and changes in the auditory ossicles. Keywords: conductive hearing loss, sensorineural hearing loss, craniofacial malformation. |
