| Title |
Complex case of congenital pulmonary sequestration with successful “EXIT” procedure |
| Authors |
Bernatavičienė, Rūta ; Pikturnaitė, Gabija ; Verkauskas, Gilvydas ; Strumila, Arūnas |
| DOI |
10.1093/jscr/rjaf1066 |
| Full Text |
|
| Is Part of |
Journal of surgical case reports.. Oxford : Oxford University Press and JSCR Publishing Ltd.. 2026, vol. 2026, iss. 1, p. [1-3].. eISSN 2042-8812 |
| Keywords [eng] |
bilateral hydrothorax ; case report ; ex utero intrapartum treatment ; exit procedure ; preterm ; pulmonary sequestration |
| Abstract [eng] |
The ex-utero intrapartum treatment (EXIT) procedure preserves fetal oxygenation via the umbilical cord in urgent respiratory distress. We report a rare case of congenital extralobar pulmonary sequestration with pedicle torsion. A 22-year-old primigravida at 29+4 weeks presented with a fetal supradiaphragmatic mass, hydrothorax, and cardiac displacement; fetal magnetic resonance imaging (MRI) confirmed pulmonary sequestration. Rapid fetal deterioration led to the termination of the pregnancy and the application of exutero intrapartum treatment procedure during Cesarean section. Before cord clamping, intubation along with thoracocentesis enabled neonatal breathing. The 2140 g newborn required intensive care for respiratory distress, heart failure, and pulmonary hypertension and was discharged stable after 3 weeks. Elective thoracoscopy at the age of 6 months removed the sequestration, confirming pedicle torsion; recovery was uneventful. This case highlights the importance of early diagnosis, multidisciplinary collaboration, and timely use of ex-utero intrapartum treatment to manage life-threatening fetal lung anomalies. |
| Published |
Oxford : Oxford University Press and JSCR Publishing Ltd |
| Type |
Journal article |
| Language |
English |
| Publication date |
2026 |
| CC license |
|
