Title Dermatofibrosarcoma protuberans in adolescence: a case report and literature review /
Translation of Title Vaikų dermatofibrosarkoma: klinikinis atvejis ir literatūros apžvalga.
Authors Valiulytė, Agnietė ; Gudavičiūtė, Milda ; Trainavičius, Kęstutis ; Šeinin, Dmitrij
DOI 10.15388/LietChirur.2015.1.5333
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Is Part of Lietuvos chirurgija.. Vilnius : Lietuvos chirurgų asociacija. 2015, T. 14, Nr. 1, p. 61-64.. ISSN 1392-0995
Keywords [eng] dermatofibrosarcoma protuberans in children ; soft tissue sarcomas ; fibrosarcomous transformation ; surgical treatment
Abstract [eng] Dermatofibrosarcoma protuberans is a very rare malignant neoplasm in children. It is reported that the classic form of dermatofibrosarcoma has a very limited metastatic potential, while a fibrosarcomous transformation of dermatofibrosarcoma protuberans has a much higher potential. We present a case of a 17-year-old boy with a huge ulcerated mass (17 x 15 cm) on his right thigh. At operation, the pathological diagnosis was dermatofibrosarcoma protuberans with a fibrosarcomous component. All lesions were removed by surgical excision with a margin of 1.5 to 3 cm. After one year, there is no evidence of tumor recurrence.
Published Vilnius : Lietuvos chirurgų asociacija
Type Journal article
Language English
Publication date 2015
CC license CC license description